A unique collection of Rombergs disease- A rare clinical entity
Journal Title: Medpulse International Journal of Pathology - Year 2018, Vol 8, Issue 1
Abstract
Background: Parry Romberg Syndrome (progressive facial hemiatrophy) is characterized by slowly progressive atrophy of subcutaneous tissue. Bones, muscles, nerves, eyes and brain may be affected by atrophy of unknown origin. This condition was first described by Romberg and Parry in 1846.Eulenberg named the disorder in the year 1872.The aim of this study is to discuss in detail the series of these cases with this rare entity at our institute and their treatment options. Methods: This is a retrospective and prospectivestudy conducted in patients treated in Plastic Surgery department at Asram Hospital. Results: Out of 9 patients studied, 5 (55.5%) were females and 4(44.4%) were males. The youngest age of the patient affected was 12 years and oldest was 34 years. The left hemiface was most commonly affected. Seven(77%) patients underwent surgery. Conclusions: Romberg’s syndrome is an extremely rare disease with threatening complications. Extensive studies on stem cells have been made to treat this disease. However, its etiopathogenesis is still unconquered.
Authors and Affiliations
K Anji Reddy, Vahini G
Keywords
Related Articles
- EP ID EP457132
- DOI 10.26611/105813
- Views 84
- Downloads 0
An unusual case of low grade endometrial stromal sarcoma in young girl - A case report
Uterine sarcomas are relatively rare tumors of mesodermal origin. They constitute 2% to 6% of uterine malignancies and occurs primarily in the 4th and 5th decades. Stromal tumours are of two types-endometrial stromal nod...
Study of endometrial histopathology inabnormal uterine bleeding
Background: Abnormal uterine bleeding is a very common gynaecological condition which can affect a women’s physical, mental and social life.The aim of the study was to evaluate the histopathological patterns of endometri...
HPLC in the diagnosis of Haemoglobinopathies and Thalassaemias
Abstract Problem statement: It is important to identify carriers of haemoglobin disorders in order to assess the risk of a couple having a severely affected child and to provide information on the options available to av...
Clinical and histopathological correlation of soft tissue tumors - A study of 150 cases
Background: Soft tissue tumors [STT] can be defined as mesenchymal proliferations that occur in the extraskeletal, nonepithelial tissue of the body, excluding the viscera, covering of the brain and lymphoreticular system...
Histopathological study of non-neoplastic and neoplastic skin lesion by punch biopsy in west India - A three year study
Background: Dermatological disorders are common in all countries but the spectrum varies greatly with wide histological variation including both benign and malignant forms. Accurate diagnosis of skin disorders is of utmo...