A Rare Seen Hemorrhage Disorder: Factor XI Deficiency Hemophilia C
Journal Title: Meandros Medical and Dental Journal - Year 2018, Vol 19, Issue 1
Abstract
Factor XI deficiency is a hemorrhage disorder which can be either autosomal recessive or/and autosomal codominant and effects both women and men. Factor XI deficiency is uncommon in non-Jewish general population and average frequency of disorder is 1/1 million. Clinical phenotype is nonhomogeneous and bleeding risk depends on individual’s reaction against hemostatic variances. There is a poor relation between the Factor XI plasma level and bleeding tendency. In case of Factor XI deficiency, uncommon, unlike hemophilia A and B, spontaneous hemorrhage, surgical or trauma sequent are at risk. Hemarthrosis and intramuscular bleeding are common in hemophilia A and B but not typically seen in Factor XI deficiency disorders. Common symptoms are easy bruising and nosebleed. History of the disorder mostly indicates the findings about the difficulty in staunching. In this case, after detecting the activated partial thromboplastin time length before the operation due to build upon mandibula, management of patients, having Factor XI deficiency hemophilia C which is a cause of rare seen hemorrhage disorder, are presented in terms of bleeding diathesis.
Authors and Affiliations
Samet Özer, Nafia Özlem Kazancı, Ergün Sönmezgöz, Şeyma Ünüvar, Nihat Akbulut
Keywords
Related Articles
- EP ID EP283442
- DOI 10.4274/meandros.2043
- Views 123
- Downloads 0
Retroperitoneal Tunneled Hemodialysis Catheter in Inferior Vena Cava: A Report of Three Cases
Finding an appropriate vascular access is difficult in long term hemodialysis patients for emergency hemodialysis. The aim of this study was to present tunneled hemodialysis catheter placement to inferior vena cava throu...
Evaluation of Color Stability and Surface Roughness of Bulk-Fill Resin Composites and Nanocomposites
Objective: The purpose of this study was to evaluate the color stability and surface roughness of four bulk-fill resin composites (SonicFill, Filtek Bulk Fill Flowable, X-tra fil, Filtek Bulk Fill Posterior) and three na...
Oxidative Alteration in Gingival Fibroblast Cells Induced By Bulk-Fill and Conventional Flowable Composites
Objective: The release of components from dental materials may cause oxidative stress which is crucial factor for tissue damage and cell apoptosis or death. The aim of this study was to evaluate the cytotoxicity of diffe...
Seropositivity of Bartonella henselae in Risky Human Population, Cats and Dogs
Objective: Bartonella species cause several diseases in humans such as cat scratch disease, bacillary angiomatosis, peliosis hepatis, endocarditis, Carrion disease and trench fever. There have been cat scratch disease an...
Cone Beam Computed Tomographic Analysis of Paranasal Variations, Osteomeatal Complex Disease, Odontogenic Lesion and Their Effect on Maxillary Sinus
Objective: The objective of this study was to establish the prevalence of nasal septal deviation, concha bullosa, and osteomeatal complex disease (obstruction), and odontogenic lesions, along with their potential relatio...