Ambras Syndrome - A Rare Congenital Entity In Pediatric Population
Journal Title: IOSR Journal of Dental and Medical Sciences (IOSR-JDMS) - Year 2017, Vol 16, Issue 11
Abstract
Ambras syndrome is a very rare type of congenital skin disease characterized by excessive hair growth on the entire body, with the exception of the palms, soles, and mucous membranes. Congenital generalized hypertrichosis associated with gingival hyperplasia are rare cases published in literature. The frequency incidence of generalized congenital hypertrichosis is about one to billions of people. Here, is a rare case report of three and half-year old girl who presented with generalized hypertrichosis with gingival fibromatosis and dysmorphic facial features is discussed
Authors and Affiliations
Layasha S, Sheela Sreedharan, Suchithra M S, Joseph T T
Keywords
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- EP ID EP238294
- DOI 10.9790/0853-1611044749
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