Aneurysm in a Large Sporadic Renal Angiomyolipoma
Journal Title: Oman Medical Journal - Year 2016, Vol 31, Issue 3
Abstract
Angiomyolipomas (AMLs) are the most common mesenchymal renal neoplasms and are classified as neoplasms of perivascular epithelioid cells (PEComa). AML is usually a benign neoplasm arising most often in the kidney although it has been described in a wide variety of sites. Most patients are adults, and one-third suffer from tuberous sclerosis. We describe a case of renal AML in a 54-year-old Bahraini woman who presented to the Bahrain Defence Force Hospital with right flank pain and hematuria, and who was known to have rheumatoid arthritis but had no cutaneous or other stigmata of tuberous sclerosis. It is the largest AML reported in Bahrain and is also striking for the fact that it contained an intratumoral aneurysm that ruptured causing symptoms leading to the radiological diagnosis of renal mass. Furthermore, the occurrence of an aneurysm in sporadic AML, as in our case, is rare since the large majority tend to be seen in association with tuberous sclerosis.
Authors and Affiliations
Bedoor Al Omran, Naseem Ansari
Keywords
Related Articles
- EP ID EP143809
- DOI 10.5001/omj.2016.42
- Views 105
- Downloads 0
The C-565T Polymorphism (rs2422493) of the ATP-binding Cassette Transporter A1 Gene Contributes to the Development and Severity of Coronary Artery Disease in an Iranian Population
Objectives: ATP-binding cassette transporter A1 (ABCA1) plays a pivotal role in reverse cholesterol transport from peripheral tissues back to the liver. Abnormalities in ABCA1 function may lead to dyslipidemia and corona...
Prevalence of Red Blood Cell Major Blood Group Antigens and Phenotypes among Omani Blood Donors
Objectives: Most literature on the frequencies of red blood cell (RBC) phenotypes are published in Europeans and Africans countries, with the frequencies in the Omani population unknown. We sought to determine the preval...
Role of Cancer Stem Cell, Apoptotic Factor, DNA Repair, and Telomerase Toward Radiation Therapy Response in Stage IIIB Cervical Cancer
Objectives: Cancer stem cells are involved in radioresistant cancers. Transcription factors Sry-related HMG box (SOX2) and octamer binding transcription factor 4 (OCT4) can confer pluripotent cell characteristics and sel...
Tuberculosis in Gulf Health Council Member States: Opportunities and Challenges Towards TB elimination
Tuberculosis (TB) is a major public health problem affecting millions of people globally. In 2016, 10.4 million people developed TB causing 1.7 million deaths. Over 95% of these deaths occurred in low- and middle-income...
Assessment of Trained Hand Hygiene Observers Using Parallel Observations
Objectives: To validate hand hygiene (HH) observers following training and determine the concordance between the observers and the Kappa index. Methods: This study was conducted during June 2017. HH observers from 15 hos...