Apical hypertrophic cardiomyopathy in an adult (RCD code: III-2A)
Journal Title: Journal of Rare Cardiovascular Diseases - Year 2016, Vol 2, Issue 6
Abstract
Apical hypertrophic cardiomyopathy (AHC) is a less common type of hypertrophic cardiomyopathy (HCM). It is characterized by typical changes in ECG (deeply inverted T waves that can mimic acute coronary syndrome), echocardiography (hypertrophy of apical segments) and ventriculography (spade-like shaped left ventricular cavity). Magnetic resonance is considered as a reference method for AHC diagnosis. We present a long follow-up period of a patient with this form of HCM. The management of patients with HCM is directed at decreasing left ventricle outflow tract narrowing (if present), decreasing of intraventricular gradient (if present), heart failure treatment and prevention of sudden cardiac death. In general treatment adequate hydration is essential and diuretics should be used with caution to prevent the increase of intraventricular gradient.
Authors and Affiliations
Kamil Bugała, Wojciech Płazak, Małgorzata Konieczyńska, Piotr Podolec
Keywords
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- EP ID EP248096
- DOI 10.20418/jrcd.vol2no6.225
- Views 113
- Downloads 0
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