Congenital Insensitivity to Pain with Anhidrosis: A Review of Literature and Case Report
Journal Title: Journal of Medical Science And clinical Research - Year 2014, Vol 2, Issue 9
Abstract
Congenital insensitivity to pain with anhidrosis is a rare genetic disorder of peripheral nervous system characterised by recurrent episode of unexplained fever, generalized anhidrosis, insensitivity to pain and temperature and self mutilating behavior. We are presenting a eight year old female with CIPA who have pus discharge and pathological fracture of anterior mandible .Sural nerve biopsy revealed reduced number of unmyelinated and small myelinated nerve fibres ,consistent with characteristic feature of CIPA.
Authors and Affiliations
Dr. Shahid Hassan
Keywords
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