Hipokalemik periyodik paralizi ile başlangıç gösteren primer Sjögren sendromu
Journal Title: Ege Tıp Dergisi - Year 2019, Vol 58, Issue 0
Abstract
Primer Sjögren sendromu (PSjS) heterojen klinik bulgularla seyreden kronik sistemik otoimmün bir hastalıktır. PSjS’de renal tutulum sıklığı %4.9 ve renal tutulum öncesi ortalama hastalık süresi iki yıl olarak bildirilmiştir. En sık renal tutulum tübülointerstisyel nefrit (TIN) olup daha az sıklıkla glomerülonefrit de görülebilmektedir. TIN bazı hastalarda izole elektrolit bozukluğu, distal renal tübüler asidoz (dRTA) yaparken bazı hastalarda ise son dönem böbrek yetmezliğine yol açabilmektedir (6). dRTA'un ise en sık klinik bulgusu hipokalemik paralizidir, bunun yanında nefrokalsinozis ve metabolik kemik hastalığına da yol açabilir. Bu yazıda PSjS’nin nadir bir başlangıç şekli olan renal tübüler asidoz ve hipokalemik periyodik paralizi olgusunu sunmaktayız.
Authors and Affiliations
Hande Ece Öz, Mete Kara, Gonca Karabulut, Yasemin Kabasakal
Keywords
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- EP ID EP670677
- DOI 10.19161/etd.648701
- Views 141
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