Incontinentia Pigmenti - Dental Manifestations: A Report of Two Cases
Journal Title: International Journal of Contemporary Medical Research - Year 2017, Vol 4, Issue 11
Abstract
Introduction: Incontinentia Pigmenti or Bloch-Sulzberger syndrome is a rare form of ectodermal dysplasia, affecting the skin, hair, eyes, central nervous system and the teeth. This variant of genodermatosis is most prevalent in females, with a reported high mortality rates in males. Case report: Dental abnormalities include hypodontia in both, the primary and permanent dentitions, peg shaped incisors and canines, and delayed eruption. This article reports the clinical features of two children, a 6 year old girl and a rare occurrence of a 12 year old boy diagnosed with Incontinentia pigmenti. Conclusion: Functional needs of such cases are usually very high, hence a multidisciplinary team is needed to achieve sufficient dental rehabilitation.
Authors and Affiliations
Neil De Souza, Jithendra Kumar, Krishna R Shetty, Paul Chalakkal
Keywords
Related Articles
- EP ID EP424095
- DOI -
- Views 136
- Downloads 0
Prevalence of Stress among Final Year MBBS Students in Kerala
Introduction: Academic stress among college students has been a topic of interest for many years. Therefore, the present study was designed to determine the prevalence of stress among final year MBBS students in Kerala....
To Compare the Quality and Duration of Analgesia by Caudal Bupivicaine and Clonidine Combination with Caudal Bupivicaine and i.v Clonidine Combination
Introduction: Regional anesthesia undertaken when the child is under general anesthesia (GA) can give prolonged analgesia in the post operative period. Caudal block since its first description in 1933 for paediatric urol...
Patient’s Awareness and Knowledge of the Root Canal Treatment in Kashmiri Population: A Survey-based Original Research
Introduction: Root canal treatment (RCT) is one of the most common endodontic procedures for which patient visits the dentist. Patients’ awareness and knowledge of the endodontic treatment is a very important issue in ev...
A Study to Assess the Prevalence of Premenstrual Syndrome and Premenstrual Dysphoric Disorder and Various Coping Strategies used by Students in A Womens Medical College from South India
Introduction: During their menstrual cycles, many women of reproductive age experience adverse physical, emotional and cognitive symptoms that often recur, usually during the luteal phase of their cycle. The constellatio...
Gauchers Disease: Case Report of 7 Rare Cases in and around Bareilly District in Northern India Over a Span of 4 Years
Introduction: Gauchers disease{GD} is a rare disease with autosomal recessive inheritance. The purpose of this study was to highlight the clinical features and diagnostic challenges observed. Material and methods: A tota...