Mal de Meleda: A Case report in Eastern india
Journal Title: IOSR Journal of Dental and Medical Sciences (IOSR-JDMS) - Year 2019, Vol 18, Issue 1
Abstract
Mal de Meleda is a rare ( Prevalence 1:1,00,000 ) autosomal recessive, diffuse, transgradient, nonsyndromic, non-epidermolytic, palmoplantar keratoderma (PPK) with associated scleroatrophy, nail changes, pseudoainhum around digits & perioral erythema without a tendency of spontaneous resolution .We present here a case of Mal de Meleda. A 10 year old male student from rural area presented with keratoderma involving palms, soles, dorsum of foot & hand along with involvement of knee & elbow. Diagnosis was confirmed by histopathological examination which showed hyperkeratosis without epidermolysis. This type of PPK may be confused with others types ( Greither’s disease,Huriez syndrome,Olmsted’s syndrome,Vohwinkal’s syndrome,Papillon Lefevre syndrome ) of PPKs & disorders of cornification.
Authors and Affiliations
Dr. Shribhagawan Rolaniya, Dr. Anand Kumar, Dr. Prof. S. S. Chaudhary, Dr. Shruti Suman
Keywords
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