Papillon-Lefevre syndrome: A case report
Journal Title: IP International Journal of Periodontology and Implantology - Year 2017, Vol 2, Issue 4
Abstract
Papillon–Lefèvre syndrome (PLS) is a rare autosomal recessive disorder which is characterized by diffuse palmoplantar keratoderma and precocious aggressive periodontitis, resulting in premature loss of deciduous and permanent dentition at a very early age. Several etiopathogenic factors are responsible for the syndrome, like immunologic alterations, genetic mutations, and also the role of microorganisms. Dentists play a major role in the diagnosis and management of PLS as there are characteristic manifestations like periodontal destruction at an early age and an early eruption of permanent teeth. Here, we are presenting an elaborate review of PLS, its etiopathogenesis, clinical presentation, and management options.
Authors and Affiliations
Nilotpol Kashyap, Brij Kumar, Mukesh Kashyap, Dharmen Bhansali
Keywords
Related Articles
- EP ID EP309126
- DOI 10.18231/2457-0087.2017.0011
- Views 75
- Downloads 0
Platelet Gel in the treatment of generalized aggressive periodontitis: A case report
Aggressive periodontitis is a less prevalent multifactorial disease which characteristically results rapid destruction of periodontium and early tooth loss This is more frequently seen in systemically healthy younger age...
A-Comparative evaluation of root surface roughness after the use of gracey curettes and piezo-surgery-driven root planning tip on root surface: An in-vitro study
Introduction and Objective The ideal instrument for initial periodontal therapy should enable the removal of all extraneous substances from the root surfaces without any iatrogenic effects Because of that the objective o...
Bone morphogenetic proteins: A strategic review
Bone morphogenetic proteins BMPs are the cytokines which play a pivotal role in embryonic patterning and initial skeletal development and also have a potent effect on bone and cartilage growth BMPs have promising prospec...
Treatment of altered passive eruption by surgical gingivectomy: A case report
In recent times, dentists, as well as patients, have developed greater awareness about the impact of teeth and gingiva in the attractiveness of smile. Short clinical crowns are considered unaesthetic and bring patients’...
Comparison of guided tissue regeneration using an equine bio-absorbable collagen membrane with equine bone graft with bovine bio-absorbable collagen membrane with bovine bone graft in the management of intrabony defects a results of 18 month
Background: Successful periodontal regeneration is considered a gold standard for periodontists. Several GTR materials and bone grafts have been attempted but showed variable success rates. Objective: The present randomi...