Papillon-Lefevre syndrome: A case report
Journal Title: IP International Journal of Periodontology and Implantology - Year 2017, Vol 2, Issue 4
Abstract
Papillon–Lefèvre syndrome (PLS) is a rare autosomal recessive disorder which is characterized by diffuse palmoplantar keratoderma and precocious aggressive periodontitis, resulting in premature loss of deciduous and permanent dentition at a very early age. Several etiopathogenic factors are responsible for the syndrome, like immunologic alterations, genetic mutations, and also the role of microorganisms. Dentists play a major role in the diagnosis and management of PLS as there are characteristic manifestations like periodontal destruction at an early age and an early eruption of permanent teeth. Here, we are presenting an elaborate review of PLS, its etiopathogenesis, clinical presentation, and management options.
Authors and Affiliations
Nilotpol Kashyap, Brij Kumar, Mukesh Kashyap, Dharmen Bhansali
Keywords
Related Articles
- EP ID EP309126
- DOI 10.18231/2457-0087.2017.0011
- Views 65
- Downloads 0
Regaining pink esthetics with Gingival Veneers – A cosmetic solution
Esthetics is a significant aspect of dentistry and the color of the gingiva, especially in the anterior region, plays an important role in overall esthetics. Gingival recession is defined as the location of the marginal...
Comparative evaluation of cryosurgery and electrosurgery in gingival depigmentation
Gingival hyperpigmentation is a major aesthetic concern for many people. Although it is not a medical problem, many people complain of dark gums as unaesthetic. Gingival depigmentation is a periodontal plastic surgical p...
Recession coverage with coronally advanced flap along with PRF membrane- A case report
Gingival recession is a common pesky problem aecting almost all middle and older aged to some degree and in patients with good oral hygiene as well as in periodontally untreated populations with poor oral hygiene Gingiva...
Bone morphogenetic proteins: A strategic review
Bone morphogenetic proteins BMPs are the cytokines which play a pivotal role in embryonic patterning and initial skeletal development and also have a potent effect on bone and cartilage growth BMPs have promising prospec...
Full mouth rehabilitation with tooth implant connection prosthesis: A case report with follow up
A Dental prosthesis that involves the combination of dental implants and natural teeth to replace missing teeth can not only increase the retention of the prosthesis but also provide good stability and aesthetic outcomes...