Prader willi syndrome- A case report
Journal Title: Indian Journal of Clinical Anaesthesia - Year 2018, Vol 5, Issue 2
Abstract
Prader willi syndrome PWS is a complex multisystem disorder PWS mainly affects central nervous system and often involves the hypothalamus Its major clinical features include neonatal hypotonia developmental delay short stature behavior abnormalities childhood onset obesity hypothalamic hypogonadism and characteristic appearanceAnaesthetic management with general or regional anaesthesia for these patients is difficult mainly due to morbid obesity The importance of PWS for anesthesiologist and primary physician is estimated by the circumstances as the prevalence of PWS is nearly as frequent as trisomy 21 We report the anaesthetic management of a 22 year old male patient with genetically proven PWS small stature obesity with characteristic behaviour problem who presented with chronic fissure in ano Though the clinical course of the patient was uneventful under saddle block In this case report we discuss our strategy for the prevention of perioperative complications for PWS patientsKeywords Prader willi syndrome
Authors and Affiliations
Shilpa H. L. , Shwetha Odeyar S. , Adarsh E. S.
Keywords
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- EP ID EP476498
- DOI 10.18231/2394-4994.2018.0057
- Views 90
- Downloads 0
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